INTESTINE Vol.20 No.3(3)

Theme Gastrointestinal polyposis -- progress in the diagnosis and treatment
Title Malignant lesions outside the colon in familial adenomatous polyposis
Publish Date 2016/05
Author Takeshi Nakajima Endoscopy Division, National Cancer Center Hospital
Author Satoru Nonaka Endoscopy Division, National Cancer Center Hospital
Author Taku Sakamoto Endoscopy Division, National Cancer Center Hospital
Author Minori Matsumoto Endoscopy Division, National Cancer Center Hospital
Author Shigeki Sekine Division of Pathology and Clinical Laboratories, National Cancer Center Hospital
Author Takeo Fukagawa 3Gastric surgery division, National Cancer Center Hospital
Author Ichiro Oda Endoscopy Division, National Cancer Center Hospital
Author Takahisa Matsuda Endoscopy Division, National Cancer Center Hospital
Author Yutaka Saito Endoscopy Division, National Cancer Center Hospital
[ Summary ] In familial adenomatous polyposis (FAP) patients, apart from colorectal lesions, lesions outside the colon, such as desmoid tumors in the stomach, duodenum (papilla, non-papilla), and small intestine are also important. After being diagnosed with FAP, a patient should undergo not only colonoscopy but also upper gastrointestinal endoscopy, abdominal computed tomography examination, and ultrasound examination of the abdomen and neck. The Spigelman classification and Church classification are beneficial for the surveillance of non-papillary duodenal tumors and desmoid tumors, respectively. Multidisciplinary clinical decision and treatment are important for surveillance in FAP patients.
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