Theme |
Dialysis and Cystic Renal Disease |
Title |
Glomerulocystic kidney disease |
Author |
Yoshio Horita |
Division of Nephrology, Department of Medicine, Nagasaki Municipal Medical Center |
Author |
Masato Tadokoro |
Division of Nephrology, Department of Medicine, Nagasaki Municipal Medical Center |
Author |
Kouichi Taura |
Division of Nephrology, Department of Medicine, Nagasaki Municipal Medical Center |
Author |
Masanobu Miyazaki |
The 2nd Department of Internal Medicine, Nagasaki University School of Medicine |
Author |
Sigeru Kohno |
The 2nd Department of Internal Medicine, Nagasaki University School of Medicine |
Author |
Takashi Harada |
Renal Care Unit, Nagasaki University School of Medicine |
[ Summary ] |
Glomerulocystic kidney disease (GCKD)was first identified in 1941, and is characterized histologically by cystic dilatation of Bowman's space and collapse of the glomerular taft. GCKD occurs primarily in neonates and children, although it is occasionally found in young adults and adults. GCKD may or may not be associated with congenital abnormalities of familial occurrence, and doubts have been raised about whether this disease is a single clinical entity. Many patients with GCKD ultimately develop renal insufficiency, but the prognosis is not always unfavorable. |